Round and spindle cells solid tumor, a morphological variants of angiosarcoma: A case report and review of the literature
Keywords:
Sarcoma, Cutaneus, Angiosarcoma, Spindle cell tumorAbstract
Soft tissue sarcomas represent a clinical and histopathological diagnostic challenge given the low incidence and high variability in clinical presentation, which often makes them unsuspected from the first consultation. A subtype that affects the skin is the idiopathic head and neck angiosarcoma, it represents less than 1% of all soft tissue sarcomas and is characterized by its aggressive biological behavior and early metastatic tendency, features that attribute an ominous prognosis to it. We report the case of a 64-year-old patient with a rapidly growing infiltrating tumor on forehead left side that initially exhibited the morphology of cutaneous lymphoma but with immunophenotyping studies, the diagnosis of cutaneous angiosarcoma was reached.
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